Natural history of vascular ring with clinical manifestations. A follow-up study of eleven unoperated cases

Scand J Thorac Cardiovasc Surg. 1977;11(1):75-7. doi: 10.3109/14017437709167818.

Abstract

A clinical follow-up study was performed in 11 unoperated patients with symptoms due to vascular ring. The age at diagnosis was 2-48 months (mean 13 months); 7 of the patients were less than 12 months old. The follow-up time varied between 1 and 22 years (median 7 years). Nine patients were entirely free of symptoms, which they had outgrown in the course of 1-2 years after the diagnosis was made; none of these 9 had symptoms after the age of 4 years. Two patients had symptoms due to either oesophageal compression or to severe associated neuromuscular lesions; the follow-up time was 3 and 1 years, respectively. Our findings lead us to support a conservative attitude regarding surgery, at least if only mild symptoms are present, If the patients can be satisfactorily treated medically, they seem to outgrow their symptoms in early childhood.

MeSH terms

  • Aortic Arch Syndromes / congenital*
  • Brachiocephalic Trunk / abnormalities*
  • Carotid Arteries / abnormalities*
  • Child, Preschool
  • Female
  • Follow-Up Studies
  • Humans
  • Hyperparathyroidism
  • Infant
  • Intellectual Disability
  • Male
  • Pulmonary Valve Stenosis
  • Subclavian Artery / abnormalities*