Hybrid Repair for Mega-Aortic Syndrome due to Giant Cell Aortitis in a Heart Failure Patient

Takehiro Inoue; Kosuke Fujii; Shigeo Kino; Shintaro Yukami; Naoya Miyashita; Hitoshi Kitayama

doi:10.3400/avd.cr.19-00096

Hybrid Repair for Mega-Aortic Syndrome due to Giant Cell Aortitis in a Heart Failure Patient

Ann Vasc Dis. 2020 Mar 25;13(1):76-80. doi: 10.3400/avd.cr.19-00096.

Authors

Takehiro Inoue¹, Kosuke Fujii², Shigeo Kino³, Shintaro Yukami², Naoya Miyashita², Hitoshi Kitayama¹

Affiliations

¹ Department of Cardiovascular Surgery, Mimihara General Hospital, Sakai, Osaka, Japan.
² Department of Cardiovascular Surgery, Kindai University Faculty of Medicine, Osakasayama, Osaka, Japan.
³ Department of Pathology, Mimihara General Hospital, Sakai, Osaka, Japan.

Abstract

The present report describes a case of mega-aortic syndrome accompanied with severe aortic regurgitation in a 75-year-old man who underwent a two-stage hybrid repair. Intraoperative pathologic findings at the first repair, consisting of Bentall operation and total arch replacement with a Lupiae graft, aided the identification of the giant cell aortitis. Despite complicating hemorrhagic stroke, steroid therapy was initiated and endovascular repair was subsequently completed. Over more than 2 years of follow-up, the patient continued steroid therapy and is doing well without any reintervention.

Keywords: giant cell aortitis; hybrid repair; mega-aortic syndrome.