Primary renal Ewing Sarcoma masquerading as Wilms in an adolescent female

Zachary M Kozel; Jennifer E Reifsnyder; Luke Griffiths; Jordan S Gitlin; Louis R Kavoussi

doi:10.1016/j.eucr.2020.101187

Primary renal Ewing Sarcoma masquerading as Wilms in an adolescent female

Urol Case Rep. 2020 Apr 8:31:101187. doi: 10.1016/j.eucr.2020.101187. eCollection 2020 Jul.

Authors

Zachary M Kozel¹, Jennifer E Reifsnyder¹, Luke Griffiths¹, Jordan S Gitlin¹, Louis R Kavoussi¹

Affiliation

¹ The Smith Institute for Urology, Zucker School of Medicine at Hofstra/Northwell, New Hyde Park, NY, USA.

Abstract

Primary renal Ewing's sarcoma (ES) of the kidney represents a rare oncologic entity belonging to the collection of small round cell tumors, which typically feature osseous presentations. Renal ES is an aggressive disease entity with high metastatic potential, either at time of presentation or following initial extirpative therapy. Herein, we report the case of a 14-year-old female who initially presented with intermittent gross painless hematuria and a large left renal mass identified on ultrasound and confirmed on follow up MRI. Following partial nephrectomy (PN), patient was diagnosed with primary renal ES and subsequently underwent completion nephrectomy and chemotherapy.

Keywords: Minimally invasive; Pediatric; Renal cell carcinoma.

Publication types

Case Reports