A Rare Report of Hypoplastic Coronary Arteries and Pulmonary Veins: A Case Report and Review of the Literature

Pediatr Cardiol. 2020 Aug;41(6):1231-1237. doi: 10.1007/s00246-020-02334-x. Epub 2020 May 2.


Congenital coronary artery anomalies are estimated to affect about 1% of the general population. Hypoplastic coronary artery disease is an uncommon subset associated with significant mortality regardless whether another major cardiac anomaly is present. In this case report, we present an extremely rare case of an infant with hypoplastic coronary artery disease and hypoplastic pulmonary veins. A literature review pertinent to the clinical findings is also contained herein.

Keywords: Diminutive coronary artery syndrome; Hypoplastic coronary artery disease; Pulmonary vein stenosis.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Angiography
  • Coronary Artery Disease / complications*
  • Coronary Artery Disease / diagnosis
  • Coronary Vessel Anomalies / complications*
  • Coronary Vessel Anomalies / diagnosis
  • Fatal Outcome
  • Female
  • Humans
  • Infant
  • Pulmonary Veins / pathology*
  • Stenosis, Pulmonary Vein / complications
  • Stenosis, Pulmonary Vein / surgery