Twiddler's syndrome with occult lead insulation damage in a child with epicardial pacemaker leads

Cardiol Young. 2020 Jun;30(6):890-891. doi: 10.1017/S1047951120001031. Epub 2020 May 19.

Abstract

We present a rare case of incidentally diagnosed Twiddler's syndrome in a child 7 years after implantation of a dual-chamber pacemaker system with epicardial leads. During revision, an insulation defect of the ventricular lead was evident, despite unremarkable prior pacemaker lead testing. The lead was repaired and a new generator was suture-fixated to prevent re-occurrence of generator manipulation.

Keywords: Twiddler’s syndrome; child; pacemaker complication.

Publication types

  • Case Reports

MeSH terms

  • Child
  • Equipment Failure*
  • Female
  • Heart Septal Defects / therapy
  • Humans
  • Incidental Findings
  • Pacemaker, Artificial / adverse effects*
  • Syndrome

Supplementary concepts

  • Atrioventricular Septal Defect