Congenital pseudarthrosis of the tibia: Results of circular external fixation treatment with intramedullary rodding and periosteal grafting technique

Acta Orthop Traumatol Turc. 2020 May;54(3):245-254. doi: 10.5152/j.aott.2020.03.26.

Abstract

Objective: This study investigated the clinical and functional results of treating congenital pseudarthrosis of the tibia (CPT) using the combined techniques of hamartoma resection, periosteal grafting, circular external fixator application, and intramedullary rodding.

Methods: The clinical and radiological data of 17 patients (mean age at the treatment time: 7.6 months (range: 4.6-9.7 months) with CPT, treated by a single surgeon between 1997 and 2017, were retrospectively analyzed. All data regarding surgical interventions, complications, deformity analysis parameters, limb length discrepancy (LLD), ankle joint range of motion, and residual deformities were reviewed. All the patients were followed up at least two years after the last surgical intervention. The mean follow-up time was 8.5 years (range: 2.2 to 15.7 years).

Results: Union was achieved with the index treatment in 15 of the 17 cases (88.2%). The mean age of the patients at the last follow-up visit was 14.2 years (range: 7.6 to 22.1). The mean LLD was 2.1 cm. Nine patients had radiological ankle valgus at the last follow-up. In the entire series, eight patients did not display any complications, four cases reported minor complications, and five cases were complicated by refractures.

Conclusion: Circular external fixator application combined with periosteal grafting is a superior method of CPT treatment. This method provides a healthy biological healing environment while correcting the mechanical problems. The combination of periosteal and cancellous bone grafts with intramedullary rods and an external fixator addresses issues that complicate obtaining and maintaining a union during the CPT treatment.

Level of evidence: Level IV, Therapeutic study.

MeSH terms

  • Adolescent
  • Bone Transplantation / methods*
  • Female
  • Follow-Up Studies
  • Fracture Fixation, Intramedullary / methods*
  • Humans
  • Ilizarov Technique*
  • Infant
  • Male
  • Outcome and Process Assessment, Health Care
  • Pseudarthrosis / congenital*
  • Pseudarthrosis / diagnosis
  • Pseudarthrosis / rehabilitation
  • Pseudarthrosis / surgery
  • Radiography / methods
  • Range of Motion, Articular
  • Recovery of Function
  • Retrospective Studies
  • Tibia* / diagnostic imaging
  • Tibia* / pathology
  • Tibia* / surgery

Supplementary concepts

  • Congenital pseudoarthrosis