Thoracic duct embolization in kaposiform lymphangiomatosis

J Vasc Surg Venous Lymphat Disord. 2020 Sep;8(5):864-868. doi: 10.1016/j.jvsv.2020.03.013. Epub 2020 Jul 9.

Abstract

An 11-year-old girl with kaposiform lymphangiomatosis presented with recurrent chylous pericardial effusions that were refractory to pericardial drainage and medical therapy. Magnetic resonance imaging demonstrated a prominent lymphatic duct with anterior mediastinal extension into the left clavicular region and a region of high signal that was favored to represent a low-flow lymphatic malformation. The patient underwent direct access thoracic duct lymphangiography with thoracic duct embolization and sclerotherapy of the large left-sided neck and pericardial lymphatic malformation. After the procedure, her pericardial effusions resolved, and she has remained asymptomatic for 15 months.

Keywords: Lymphatic malformation; Sclerotherapy; Thoracic duct embolization; Vascular anomaly.

Publication types

  • Case Reports

MeSH terms

  • Child
  • Embolization, Therapeutic*
  • Female
  • Humans
  • Lymphangiectasis / diagnostic imaging
  • Lymphangiectasis / therapy*
  • Lymphatic Abnormalities / diagnostic imaging
  • Lymphatic Abnormalities / therapy*
  • Pericardial Effusion / diagnostic imaging
  • Pericardial Effusion / therapy*
  • Sclerotherapy*
  • Thoracic Duct* / diagnostic imaging
  • Treatment Outcome