Differential Diagnoses of Inclusion Body Myositis

Neurol Clin. 2020 Aug;38(3):697-710. doi: 10.1016/j.ncl.2020.03.014.

Abstract

Inclusion body myositis is a slowly progressive myopathy, characteristically affecting quadriceps and long finger flexors. Atypical presentations do occur, however, and there is overlap with other myopathies, including inflammatory and hereditary etiologies. This article discusses atypical cases and differential diagnoses and considers the role of imaging and histopathology in differentiating inclusion body myositis.

Keywords: Diagnosis; Inclusion body myositis; Inflammatory myopathy; Magnetic resonance imaging; Muscle biopsy; Muscular dystrophy.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't
  • Review

MeSH terms

  • Aged
  • Diagnosis, Differential
  • Humans
  • Male
  • Middle Aged
  • Muscle, Skeletal / diagnostic imaging*
  • Muscle, Skeletal / pathology
  • Muscular Dystrophies / diagnostic imaging
  • Myositis / diagnostic imaging
  • Myositis / pathology
  • Myositis, Inclusion Body / diagnostic imaging*
  • Myositis, Inclusion Body / pathology