A 5-year-old black female, the youngest patient so far reported, presented with osseous choristoma of the tongue. The lesion was located on the dorsum of the posterior tongue at the circumvallate papillae area. The origin of the tumor is unknown; however, ossification of remnants of the branchial arches is accepted by most authorities. The tumor was pedunculated with no associated symptoms, and its excision was not followed by recurrence to date.