Secondary Extra-Articular Synovial Osteochondromatosis with Involvement of the Leg, Ankle and Foot. An Exceptional Case

Reumatol Clin (Engl Ed). 2020 Aug 11:S1699-258X(20)30163-7. doi: 10.1016/j.reuma.2020.07.003. Online ahead of print.
[Article in English, Spanish]

Abstract

Extraarticular synovial osteochondromatosis is a very rare benign disease whose aetiology may be primary or secondary to pre-existing pathology or after trauma. The diagnosis can be made with plain radiography and CT, and MRI is necessary to evaluate the non-mineralized soft tissue component and assess extension. It must be confirmed with a pathological study by biopsy or resection. There is up to a 5% chance of malignant transformation. The treatment of choice for the extensive extra-articular form is surgery by open resection. The case presented illustrates an atypical form of secondary extraarticular OCS with multiple involvement of the leg, ankle and foot.

Keywords: Extraarticular; Osteochondromatosis; Osteocondromatosis; Radiology; Radiología; Reumatología; Rheumatology; Sinovial; Synovial.

Publication types

  • Case Reports