Intracardiac paragangliomas: surgical approach and perioperative management

Gen Thorac Cardiovasc Surg. 2021 Mar;69(3):555-559. doi: 10.1007/s11748-020-01503-2. Epub 2020 Oct 19.


Intracardiac paragangliomas most commonly arise from the left atrium and are often infiltrative and densely adherent to surrounding structures. Given their rarity, only scattered reports exist in the literature and standardized perioperative and surgical management is not well established. We describe a case of a 60-year-old woman with a mildly functioning intracardiac paraganglioma in which division of the superior vena cava improved exposure and enabled a complex limited resection. Further, we provide an overview of the diagnostic workup, perioperative medical management, surgical approach, and surveillance strategy in patients with these challenging tumors.

Keywords: Cardiac tumor; Intracardiac paraganglioma; Mediastinal mass; SDHC mutation.

Publication types

  • Case Reports

MeSH terms

  • Female
  • Humans
  • Middle Aged
  • Paraganglioma*
  • Vena Cava, Superior*