Peripheral Nervous System Involvement

Hematol Oncol Clin North Am. 2020 Dec;34(6):1091-1098. doi: 10.1016/j.hoc.2020.07.004. Epub 2020 Sep 10.

Abstract

Peripheral nervous system involvement in primary systemic amyloidosis is another important organ involvement in the spectrum of this disease entity. Early recognition may lead to an earlier diagnosis and treatment with improvement in prognosis.

Keywords: AL amyloidosis; Amyloid autonomic neuropathy; Amyloid myopathy; Amyloid neuropathy; Amyloidosis; Light chain amyloid; Primary systemic.

Publication types

  • Review

MeSH terms

  • Humans
  • Immunoglobulin Light-chain Amyloidosis* / complications
  • Immunoglobulin Light-chain Amyloidosis* / diagnosis
  • Immunoglobulin Light-chain Amyloidosis* / metabolism
  • Immunoglobulin Light-chain Amyloidosis* / therapy
  • Peripheral Nervous System / metabolism*
  • Peripheral Nervous System Diseases* / diagnosis
  • Peripheral Nervous System Diseases* / etiology
  • Peripheral Nervous System Diseases* / metabolism
  • Peripheral Nervous System Diseases* / therapy