Congenital atresia of the left main coronary artery: management of a 5-year-old child in extremis

Martin Schmiady; Oliver Kretschmar; René Prêtre; Hitendu Dave

doi:10.1093/icvts/ivaa268

Congenital atresia of the left main coronary artery: management of a 5-year-old child in extremis

Interact Cardiovasc Thorac Surg. 2021 Apr 8;32(3):497-498. doi: 10.1093/icvts/ivaa268.

Authors

Martin Schmiady^{1

2}, Oliver Kretschmar³, René Prêtre^{1

2

4

5}, Hitendu Dave^{1

2}

Affiliations

¹ Division of Congenital Cardiovascular Surgery, University Children's Hospital Zurich, Zurich, Switzerland.
² Department of Cardiac Surgery, University Heart Center, University Hospital Zurich, Zurich, Switzerland.
³ Division of Paediatric Cardiology, University Children's Hospital Zurich, Zurich, Switzerland.
⁴ Department of Cardiac Surgery, Centre Hospitalier Universitaire Vaudois (CHUV), Lausanne, Switzerland.
⁵ Clinique des Grangettes, Geneva, Switzerland.

Abstract

Atresia of the left main coronary artery is a rare coronary anomaly. We describe the case of a 5-year-old child presenting in emergency in extremis. Clinical findings of haemodynamic collapse, malignant ventricular tachyarrhythmias and severe mitral regurgitation were indicative of a possible ischaemic aetiology. Surgical revascularization of the atretic left main coronary artery segment using an interposition autologous saphenous vein graft was successfully performed.

Keywords: Coronary artery anomalies; Coronary artery bypass grafting; Left main coronary artery atresia; Mitral regurgitation.

Publication types

Case Reports

MeSH terms

Child, Preschool
Coronary Angiography / methods
Coronary Vessel Anomalies / complications
Coronary Vessel Anomalies / diagnostic imaging
Coronary Vessel Anomalies / surgery*
Humans
Male
Saphenous Vein / transplantation*
Tachycardia, Ventricular / diagnostic imaging
Tachycardia, Ventricular / etiology
Tachycardia, Ventricular / surgery*
Vascular Surgical Procedures / methods*