Linear Scleroderma and Primary Sclerosing Cholangitis: An Undescribed Association

Iñigo Navarro Fernández; Susana Armesto Alonso; Carlos Duran Vian; L Reguero Del Cura; Carmen González-Vela; Marcos González-López

doi:10.4103/ijd.IJD_473_18

Linear Scleroderma and Primary Sclerosing Cholangitis: An Undescribed Association

Indian J Dermatol. 2020 Nov-Dec;65(6):514-515. doi: 10.4103/ijd.IJD_473_18.

Authors

Iñigo Navarro Fernández¹, Susana Armesto Alonso¹, Carlos Duran Vian¹, L Reguero Del Cura¹, Carmen González-Vela², Marcos González-López¹

Affiliations

¹ Department of Dermatology, Hospital Universitario Marqués de Valdecilla, Santander, Spain.
² Department of Pathology, Hospital Universitario Marqués de Valdecilla, Santander, Spain.

Abstract

Linear scleroderma (LS) is clinically characterized by the presence of sclerotic areas of skin, which develop in a linear pattern. Primary sclerosing cholangitis is a cholestatic disorder that can lead to end-stage liver disease. We present, for the first time in English literature, the case of a patient suffering from both the diseases. This highlights the fact that, even though LS has conventionally been considered to be a form of localized scleroderma, this does not necessarily imply that it is an exclusively cutaneous disease.

Keywords: Linear scleroderma; morphea; primary sclerosing cholangitis.

Publication types

Case Reports