Extranodal blastoid/pleomorphic variant of mantle cell lymphoma involving the testis and skin

BMJ Case Rep. 2021 Jan 28;14(1):e239014. doi: 10.1136/bcr-2020-239014.

Abstract

We report a case of extranodal mantle cell lymphoma of the testis in a 72-year-old Caucasian man who presented to his physician's office with rapidly enlarging left testicular mass and skin lesions which were subsequently biopsy-proven to be mantle cell lymphoma. We discuss the clinicopathological features and current management in relapsed and refractory settings of this rare presentation of mantle cell lymphoma.

Keywords: dermatology; malignant and benign haematology; urology.

Publication types

  • Case Reports

MeSH terms

  • Aged
  • Antibodies, Monoclonal, Humanized / therapeutic use
  • Antineoplastic Combined Chemotherapy Protocols / therapeutic use
  • Cisplatin / therapeutic use
  • Cyclophosphamide / therapeutic use
  • Cytarabine / therapeutic use
  • Dexamethasone / therapeutic use
  • Doxorubicin / therapeutic use
  • Humans
  • In Situ Hybridization, Fluorescence
  • Lenalidomide / therapeutic use
  • Lymphoma, Mantle-Cell / genetics
  • Lymphoma, Mantle-Cell / pathology*
  • Lymphoma, Mantle-Cell / therapy
  • Male
  • Oncogene Proteins, Fusion / genetics
  • Orchiectomy
  • Positron-Emission Tomography
  • Prednisone / therapeutic use
  • Proto-Oncogene Proteins c-myc / genetics
  • Radiotherapy
  • Rituximab / therapeutic use
  • Skin Neoplasms / genetics
  • Skin Neoplasms / pathology*
  • Skin Neoplasms / therapy
  • Testicular Neoplasms / genetics
  • Testicular Neoplasms / pathology*
  • Testicular Neoplasms / therapy
  • Vincristine / therapeutic use

Substances

  • Antibodies, Monoclonal, Humanized
  • IGH-CCND1 fusion protein, human
  • MYC protein, human
  • Oncogene Proteins, Fusion
  • Proto-Oncogene Proteins c-myc
  • R-CHOP protocol
  • Cytarabine
  • Rituximab
  • Vincristine
  • Dexamethasone
  • Doxorubicin
  • Cyclophosphamide
  • Lenalidomide
  • obinutuzumab
  • Cisplatin
  • Prednisone

Supplementary concepts

  • DHAP protocol