Cutaneous Sarcomas

Otolaryngol Clin North Am. 2021 Apr;54(2):369-378. doi: 10.1016/j.otc.2020.11.010. Epub 2021 Feb 16.


Cutaneous sarcomas represent a rare group of tumors presenting in the head and neck. In this article, we discuss specific sarcoma tumor types and their presentation, pathogenesis, histologic findings, and management recommendations. Tumors to be reviewed include dermatofibrosarcoma protuberans, atypical fibroxanthoma, pleomorphic dermal sarcoma, cutaneous leiomyosarcoma, and angiosarcoma.

Keywords: Angiosarcoma; Atypical fibroxanthoma; Cutaneous; Dermatofibrosarcoma protuberans; Leiomyosarcoma; Pleomorphic dermal sarcoma; Sarcoma; Surgery for cutaneous sarcoma.

Publication types

  • Review

MeSH terms

  • Humans
  • Sarcoma* / diagnosis
  • Sarcoma* / therapy
  • Skin Neoplasms* / therapy