Abstract
The medical and surgical management of the chronic and recurrent esophageal and anal lesions of recessive dystrophic epidermolysis bullosa pose challenging problems for the physician. Various therapeutic approaches are discussed, and the case histories of four problem patients are reviewed.
MeSH terms
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Adolescent
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Adult
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Anus Diseases / etiology
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Anus Diseases / therapy
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Child
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Colon / transplantation
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Deglutition Disorders / drug therapy
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Deglutition Disorders / etiology*
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Deglutition Disorders / surgery
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Dexamethasone / therapeutic use
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Dilatation
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Epidermolysis Bullosa / complications*
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Epidermolysis Bullosa / therapy
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Esophageal Diseases / etiology*
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Esophageal Diseases / therapy
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Esophagus / surgery
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Female
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Humans
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Infant
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Male
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Prednisone / therapeutic use