Adult-onset en coup de sabre scleroderma in a patient with linear localized scleroderma profunda: A case report and literature review

SAGE Open Med Case Rep. 2021 Mar 19;9:2050313X21993304. doi: 10.1177/2050313X21993304. eCollection 2021.

Abstract

The en coup de sabre variant of linear scleroderma typically occurs in children. We report a unique case of adult-onset en coup de sabre scleroderma in a patient with linear localized scleroderma profunda. The patient was treated with oral steroids and oral methotrexate improving her cutaneous disease. This case highlights the importance of a thorough cutaneous examination as this adult patient developed an entity traditionally believed to occur in childhood.

Keywords: Scleroderma; adult-onset scleroderma; en coup de sabre scleroderma; linear scleroderma; localized scleroderma; morphea.

Publication types

  • Case Reports