Total Anomalous Pulmonary Venous Connection and Aortopulmonary Window: Successful Management of a Rare Association

World J Pediatr Congenit Heart Surg. 2021 Nov;12(6):785-787. doi: 10.1177/2150135120957947. Epub 2021 May 10.


The association of total anomalous pulmonary venous connection (TAPVC) with aortopulmonary window (APW) is extremely rare. The coexistence of these two anomalies will have implications on clinical presentation, diagnosis, and pathophysiology. The lungs are exposed to pulmonary venous hypertension due to obstructed TAPVC as well as pulmonary arterial hypertension due to unrestrictive APW. We describe successful management of this unusual association in a three-month-old child.

Publication types

  • Case Reports

MeSH terms

  • Aortopulmonary Septal Defect* / diagnostic imaging
  • Aortopulmonary Septal Defect* / surgery
  • Humans
  • Infant
  • Pulmonary Arterial Hypertension*
  • Pulmonary Veins* / diagnostic imaging
  • Pulmonary Veins* / surgery
  • Scimitar Syndrome* / diagnostic imaging
  • Scimitar Syndrome* / surgery