Large, Hormonally Active Primary Cardiac Paraganglioma: Diagnosis and Management

Ann Thorac Surg. 2022 Mar;113(3):e167-e170. doi: 10.1016/j.athoracsur.2021.05.042. Epub 2021 Jun 8.

Abstract

We describe a 26-year-old woman presenting with chest pain and evidence of coronary ischemia. Echocardiography revealed a large left ventricular mass initially deemed unresectable at her initial institution. Investigation revealed a dopamine-secreting primary cardiac paraganglioma encompassing vital cardiac architecture. This case discusses our heart team approach to complex cardiac masses and illustrates the feasibility of surgical resection in complex cases of hormonally active primary cardiac paragangliomas.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Chest Pain
  • Female
  • Heart Neoplasms* / diagnosis
  • Heart Neoplasms* / surgery
  • Humans
  • Paraganglioma* / diagnostic imaging
  • Paraganglioma* / surgery
  • Paraganglioma, Extra-Adrenal*
  • Tomography, X-Ray Computed