Retroperitoneal Lympathic Malformations as First Presentation of Lymphangioleiomyomatosis

Abstract

Teaching Point: This case highlights the extrapulmonary lymphatic abnormalities that may be associated with pulmonary lymphangioleiomyomatosis.

Keywords: cystic abdominal mass; lymphangioleiomyomatosis; lymphatic malformation; mediastinum; retroperitoneum.