The treatment dilemma in adult patients with peripheral pulmonary artery stenosis of diverse etiologies

Egypt Heart J. 2021 Jul 15;73(1):65. doi: 10.1186/s43044-021-00190-5.

Abstract

Background: Peripheral pulmonary artery stenosis (PPAS) is a rare and underdiagnosed phenomenon that is reported infrequently in adult patients. Most patients with PPAS have concomitant congenital heart diseases, a history of palliative surgical therapies during childhood, or syndromic characteristics. Acquired cases are rare, and they are underestimated in adulthood and managed inappropriately.

Case presentation: This case series describes 3 adult patients with PPAS of diverse etiologies and discusses their underlying causes, diagnostic modalities, and treatment strategies.

Conclusions: In patients with PPAS, sufficient heed should be paid to endovascular interventions such as balloon dilation and primary or bailout stenting, not least vis-à-vis the type and size of balloons or stents as well as complications and preventive strategies.

Keywords: Balloon angioplasty; Diagnostic modalities; Endovascular intervention; Peripheral pulmonary artery stenosis; Stenting; Treatment approach.