Speech Perception and Production in Cochlear Implant Recipients with Pendred Syndrome

Balkan Med J. 2021 Jul;38(4):244-248. doi: 10.5152/balkanmedj.2021.20182.


Aims: Patients with the Pendred syndrome suffer very often from a hearing loss. They may be good candidates for a cochlear implantation, but unfortunately, due to the fluctuating character of the hearing loss, they may escape such indication. In the study, we compared speech production and speech acquisition in 2 groups of implanted patients: those with the Pendred syndrome, and standard non-syndromic patients.

Methods: Ten patients with Pendred syndrome were analyzed for speech perception and production. The control group consisted of 41 non-syndromic implanted patients. All implantees were scored according to speech perception, speech production, and the sum of both. The data were statistically analyzed.

Results: No statistical difference was found in language acquisition and production in implantees with Pendred syndrome when compared to non-syndromic patients with cochlear implants. Nor there was any difference in speech production and acquisition between the 2 compared groups regarding surgical age, time elapsed after surgery, or age during the testing.

Conclusion: In this study evaluating language and speech production and acquisition, patients with Pendred syndrome who underwent cochlear implants show comparable results to their implanted peers with deafness of a different etiology.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Child
  • Child, Preschool
  • Cochlear Implants / standards*
  • Female
  • Goiter, Nodular / complications
  • Goiter, Nodular / psychology
  • Goiter, Nodular / surgery*
  • Hearing Loss / etiology
  • Hearing Loss / surgery
  • Hearing Loss, Sensorineural / complications
  • Hearing Loss, Sensorineural / psychology
  • Hearing Loss, Sensorineural / surgery*
  • Humans
  • Male
  • Speech Perception / physiology*

Supplementary concepts

  • Pendred syndrome