A Rare Case of Severe Nontropical Isolated Right Ventricular Endomyocardial Fibrosis

Shaaheen Laher; Yee Weng Wong; David Platts; Anil Prabhu; Bruce Thomson; Christian Hamilton-Craig; David Godbolt; Elizabeth Cheesman; Alexander Dashwood

doi:10.1016/j.jaccas.2020.09.042

A Rare Case of Severe Nontropical Isolated Right Ventricular Endomyocardial Fibrosis

JACC Case Rep. 2020 Nov 18;2(13):2078-2084. doi: 10.1016/j.jaccas.2020.09.042. eCollection 2020 Nov.

Authors

Shaaheen Laher¹, Yee Weng Wong^{1

2}, David Platts^{1

3}, Anil Prabhu¹, Bruce Thomson¹, Christian Hamilton-Craig³, David Godbolt¹, Elizabeth Cheesman², Alexander Dashwood^{1

2}

Affiliations

¹ Heart Lung Institute, The Prince Charles Hospital, Chermside, Australia.
² Cardio-Vascular Molecular & Therapeutics Translational Research Group, University of Queensland, Brisbane, Australia.
³ Cardiology Program, The Prince Charles Hospital School of Medicine, University of Queensland School of Medicine, Griffith University, Brisbane, Australia.

Abstract

We present a case of late presentation nontropical endomyocardial fibrosis isolated to the right ventricle and tricuspid valve (TV). In response to deteriorating hemodynamics, surgical debulking and TV removal were performed before initiation of centralized venoarterial extracorporeal membrane oxygenation support. Definitive endomyocardial resection with a TV prosthesis was then successfully completed. (Level of Difficulty: Advanced.).

Keywords: CE, contrast-enhanced; CMR, cardiac magnetic resonance; ECMO, extracorporeal membrane oxygenation; EMF, endomyocardial fibrosis; LV, left ventricular; RA, right atrial; RV, right ventricular; RVOT, right ventricular outflow tract; TTE, Transthoracic echocardiogram; TV, tricuspid valve; contrast enhanced TTE; endomyocardial fibrosis; right ventricle.

Publication types

Case Reports