Berry syndrome-a rare congenital cardiac anomaly

Indian J Thorac Cardiovasc Surg. 2021 Sep;37(5):526-532. doi: 10.1007/s12055-021-01206-0. Epub 2021 Jun 8.

Abstract

Berry syndrome is a rare congenital cardiac anomaly, characterized by distal aortopulmonary window, hypoplasia or interruption of the aortic arch, intact ventricular septum, and aortic origin of the right pulmonary artery and patent ductus arteriosus. Anatomic depiction of each component is important for the diagnosis. Single-stage surgical repair is challenging but feasible with good survival outcomes. The available literature on this anomaly is limited. Hence, this paper aims at reviewing the literature on Berry syndrome.

Keywords: Aortopulmonary window; Berry syndrome; Interrupted aortic arch; Right pulmonary artery.

Publication types

  • Review