Pre-Epiglottic Baton Plate in the Management of Upper Airway Obstruction in an Infant with Femoral Facial Syndrome: A Case Report

Cleft Palate Craniofac J. 2023 Mar;60(3):367-375. doi: 10.1177/10556656211059705. Epub 2021 Nov 17.

Abstract

Femoral facial syndrome (FFS) is a rare condition which may present with hypoplasia or aplasia of the femora and unusual facies characterized by long philtrum, thin upper lip and micrognathia. We present the case of a ten-month old infant with FFS who had retroglossal obstruction and who was treated with a pre-epiglottic baton plate. The pre-epiglottic baton plate can be a simple, non-invasive and effective tool for the clinical management of syndromic patients with mild-to-moderate upper airway obstruction due to micrognathia.

Keywords: case report; femoral facial syndrome; pre-epiglottic baton plate; upper airway obstruction.

Publication types

  • Case Reports

MeSH terms

  • Airway Obstruction* / diagnostic imaging
  • Airway Obstruction* / etiology
  • Airway Obstruction* / surgery
  • Femur
  • Humans
  • Infant
  • Micrognathism* / diagnostic imaging
  • Micrognathism* / surgery
  • Pierre Robin Syndrome* / complications
  • Pierre Robin Syndrome* / therapy

Supplementary concepts

  • Femoral facial syndrome