Presentation and Management of Atypical Orofacial Clefts: A Single-Institution Experience for 13 Year Period

Cleft Palate Craniofac J. 2023 Feb;60(2):133-141. doi: 10.1177/10556656211055012. Epub 2021 Nov 17.


This study reviews the craniofacial clefts that presented at a Nigerian tertiary health facility, highlighting our experience with the pattern of presentation and surgical care of these patients.

A retrospective review of the smile train database and medical records of all individuals who had been diagnosed with any of the Tessier craniofacial clefts and managed between 1st January 2007 and 31st December 2020 was done. The data were presented as numbers and percentages of cases.

The cleft clinic of a tertiary health facility and a major cleft referral center in South-West Nigeria.

Forty-five patients with craniofacial clefts were managed over the study period. 15.6% had associated syndromes, 2.2% had a family history of similar craniofacial cleft and 11% had a history of a possible teratogen. There were 21 (46.7%) middle clefts, 14(31.1%) lateral clefts and 10(22.2%) oblique clefts. The most common type of cleft was Tessier 0 while the Tessier 6 was the least common type. The median age at surgery was 10 months for male and 5months for female subjects, 15.3% complication rate was found in this study. Four patients had revision surgeries to correct residual deformities in this study.

The diverse presentations and occurrence of the rare craniofacial clefts present complex aesthetic and functional problems that require individualized often multidisciplinary care. The execution of a properly planned treatment will reduce complications and the need for revision surgeries.

Keywords: craniofacial clefts; laterality; rare; surgical repair.

MeSH terms

  • Cleft Lip* / surgery
  • Cleft Palate* / surgery
  • Esthetics, Dental
  • Facial Expression
  • Female
  • Health Facilities
  • Humans
  • Male