Ebstein's Anomaly, Left Ventricular Noncompaction and Gerbode-Like Defect Triad (Fetal Diagnosis and Neonatal Course)

Mohammad Mehdi; Snigdha Bhatia; Mehul Patel; Ashraf Aly

doi:10.1155/2021/9969588

Ebstein's Anomaly, Left Ventricular Noncompaction and Gerbode-Like Defect Triad (Fetal Diagnosis and Neonatal Course)

Case Rep Pediatr. 2021 Nov 11:2021:9969588. doi: 10.1155/2021/9969588. eCollection 2021.

Authors

Mohammad Mehdi¹, Snigdha Bhatia¹, Mehul Patel², Ashraf Aly^{1

3}

Affiliations

¹ Department of Pediatrics, University of Texas Medical Branch, Galveston, TX 77555, USA.
² Division of Pediatric Cardiology, University of Texas Health McGovern Medical School, Houston, TX 77030, USA.
³ Division of Pediatric Cardiology, University of Texas Medical Branch, Galveston, TX 77555, USA.

Abstract

Ebstein's anomaly is characterized by the apical displacement of the septal and posterior leaflets of the tricuspid valve with atrialization of the right ventricle (RV). It is commonly associated with other heart defects including left ventricular noncompaction. We describe a case of prenatally diagnosed Ebstein's anomaly in association with left ventricular noncompaction and a septal defect between the left ventricle and the atrialized portion of the RV (Gerbode-like defect). The patient underwent a modified Blalock-Taussig shunt followed by Glenn procedure because of severe RV hypoplasia and RV outflow tract obstruction. The patient tolerated both procedures and is doing clinically well in anticipation of Fontan procedure for single ventricle palliation.

Publication types

Case Reports