The asymmetric Pitx2 gene regulates gut muscular-lacteal development and protects against fatty liver disease

Cell Rep. 2021 Nov 23;37(8):110030. doi: 10.1016/j.celrep.2021.110030.

Abstract

Intestinal lacteals are essential lymphatic channels for absorption and transport of dietary lipids and drive the pathogenesis of debilitating metabolic diseases. However, organ-specific mechanisms linking lymphatic dysfunction to disease etiology remain largely unknown. In this study, we uncover an intestinal lymphatic program that is linked to the left-right (LR) asymmetric transcription factor Pitx2. We show that deletion of the asymmetric Pitx2 enhancer ASE alters normal lacteal development through the lacteal-associated contractile smooth muscle lineage. ASE deletion leads to abnormal muscle morphogenesis induced by oxidative stress, resulting in impaired lacteal extension and defective lymphatic system-dependent lipid transport. Surprisingly, activation of lymphatic system-independent trafficking directs dietary lipids from the gut directly to the liver, causing diet-induced fatty liver disease. Our study reveals the molecular mechanism linking gut lymphatic function to the earliest symmetry-breaking Pitx2 and highlights the important relationship between intestinal lymphangiogenesis and the gut-liver axis.

Keywords: ASE enhancer; Pitx2; dietary lipid transport; fatty liver disease; gut lymphatic development; lacteal; left-right asymmetry; oxidative stress; portal lipid transport; villus-axial smooth muscle.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Biological Transport
  • Dietary Fats / metabolism*
  • Duodenum / metabolism
  • Female
  • Homeobox Protein PITX2
  • Homeodomain Proteins / genetics
  • Homeodomain Proteins / metabolism*
  • Intestinal Mucosa / metabolism
  • Intestines / metabolism*
  • Lipid Metabolism / physiology
  • Lipids / physiology
  • Lymphangiogenesis / physiology
  • Lymphatic Vessels / metabolism
  • Male
  • Mice
  • Signal Transduction
  • Transcription Factors / genetics
  • Transcription Factors / metabolism*

Substances

  • Dietary Fats
  • Homeodomain Proteins
  • Lipids
  • Transcription Factors