Dental Anomalies in Parry-Romberg Syndrome: A 40-Year Retrospective Review

Cleft Palate Craniofac J. 2023 Aug;60(8):956-961. doi: 10.1177/10556656221086174. Epub 2022 Mar 14.

Abstract

Objective: This study investigates crown and root anomalies in patients with Parry-Romberg Syndrome.

Design: This is a retrospective review of patients with Parry-Romberg Syndrome who were evaluated at a tertiary care center from 1980-2020.

Setting: Patients seen in the dental unit from 1980-2020.

Patients, participants: Seventeen patients with documented Parry-Romberg Syndrome were referred for dental evaluation.

Main outcome measures: All dental anomalies were documented. Root anomalies were assessed using panoramic radiographs and cone beam CT (CBCT) scans to evaluate buccal-lingual, mesio-distal, and axial measurements of hypoplastic teeth, which were compared to those of contralateral teeth.

Results: Findings included agenesis (29%, n = 5), hypoplastic teeth (29%, n = 5), delayed canine eruption (24%, n = 4), and mulberry molars (12%, n = 2). Of the five patients with tooth hypoplasia, four had CBCT records and the fifth had panoramic radiographs available for assessment. Axial length was always shorter in hypoplastic teeth relative to contralateral teeth, with differences ranging from 1.2-9.2 mm. Differences in crown size of hypoplastic versus contralateral teeth were unpredictable but always present.

Conclusions: Patients with Parry-Romberg Syndrome can have hypoplastic roots with atypical crown morphology. A patient's specific dental anomaly will influence planning and treatment.

Keywords: Parry-Romberg Syndrome; hemifacial atrophy; root hypoplasia.

MeSH terms

  • Cone-Beam Computed Tomography
  • Facial Hemiatrophy*
  • Humans
  • Radiography, Panoramic
  • Retrospective Studies