Scattered Media Elastic Fibers from the Aortic Root to the Ascending Aorta in a 30-Year-Old Marfan Syndrome Patient

Tomohiro Nakajima; Yutaka Iba; Syuichi Naraoka; Tsuyoshi Shibata; Shintaro Sugita; Nobuyoshi Kawaharada

doi:10.5761/atcs.cr.22-00044

Scattered Media Elastic Fibers from the Aortic Root to the Ascending Aorta in a 30-Year-Old Marfan Syndrome Patient

Ann Thorac Cardiovasc Surg. 2024 Jan 25;30(1):22-00044. doi: 10.5761/atcs.cr.22-00044. Epub 2022 May 19.

Authors

Tomohiro Nakajima¹, Yutaka Iba¹, Syuichi Naraoka¹, Tsuyoshi Shibata¹, Shintaro Sugita², Nobuyoshi Kawaharada¹

Affiliations

¹ Department of Cardiovascular Surgery, Sapporo Medical University School of Medicine, Sapporo, Hokkaido, Japan.
² Department of Surgical Pathology, Sapporo Medical University School of Medicine, Sapporo, Hokkaido, Japan.

Abstract

We present a case report of a 30-year-old Marfan syndrome patient who underwent a David procedure for severe aortic valve insufficiency and Valsalva aneurysm. Harvested aortic walls were examined by pathologists. Although the tunica media of the ascending aorta contained aligned elastic fibers, the aortic root media lacked aligned elastic fibers.

Keywords: Marfan syndrome; aortic root dilation; elastic fiber.

Publication types

Case Reports

MeSH terms

Adult
Aorta, Thoracic
Aortic Aneurysm* / diagnostic imaging
Aortic Aneurysm* / etiology
Aortic Aneurysm* / surgery
Aortic Valve / diagnostic imaging
Aortic Valve / surgery
Elastic Tissue
Humans
Marfan Syndrome* / complications
Marfan Syndrome* / diagnosis
Marfan Syndrome* / surgery
Treatment Outcome