Eisenmenger Syndrome in Case of Extended Goldenhar Complex Treated With Heart-Lung Transplantation

Cesar A Keller; Francisco G Alvarez

doi:10.1016/j.jaccas.2022.05.001

Eisenmenger Syndrome in Case of Extended Goldenhar Complex Treated With Heart-Lung Transplantation

JACC Case Rep. 2022 Jun 15;4(12):699-703. doi: 10.1016/j.jaccas.2022.05.001.

Authors

Cesar A Keller¹, Francisco G Alvarez¹

Affiliation

¹ Division of Lung Transplant, Department of Transplantation, Mayo Clinic, Jacksonville, Florida, USA.

Abstract

A patient diagnosed with expanded Goldenhar complex with oculoauriculovertebral spectrum complicated with complex pulmonary and congenital heart disease, underwent successful heart-lung transplantation 21 years ago, with excellent functional outcome and good quality of life. Heart-lung transplantation can be an option of care for patients with expanded Goldenhar complex. (Level of Difficulty: Advanced.).

Keywords: CHD, congenital heart disease; EGC, expanded Goldenhar complex; FEV1, forced expiratory volume in first second of expiration; FVC, forced vital capacity; HLT, heart-lung transplantation; PDA, patent ductus arteriosus; POD, postoperative day; congenital heart defect; genetic disorders; pulmonary atresia; pulmonary hypertension.

Publication types

Case Reports