Microcystic lymphatic malformation presenting as firm, skin-colored papules of the lips

Pediatr Dermatol. 2022 Nov;39(6):992-994. doi: 10.1111/pde.15060. Epub 2022 Jun 23.


Microcystic lymphatic malformation (MiLM), also known as lymphangioma circumscriptum, is a superficial collection of lymphatic vessels measuring <1 cm in the largest diameter, often with a more extensive deeper malformation. It commonly presents as discrete or grouped plaques of clear or hemorrhagic vesicles classically described as "frogspawn"; however, here we describe a case of its unique presentation as firm papules on the lips of a healthy six-year-old child. These skin-colored papules in the absence of vesicles with lymphatic and/or hemorrhagic fluid may not be clinically indicative of MiLM. This case represents a diagnostic challenge due to the unique morphology of pink, fleshy papules as opposed to the clear or hemorrhagic vesicles typically observed in MiLM.

Keywords: laser; vascular malformation.

Publication types

  • Case Reports

MeSH terms

  • Blister
  • Child
  • Cysts*
  • Hemorrhage
  • Humans
  • Lip
  • Lymphangioma* / diagnosis
  • Lymphatic Abnormalities* / diagnosis