Ivacaftor, not ivacaftor/lumacaftor, associated with lower pulmonary inflammation in preschool cystic fibrosis

Pediatr Pulmonol. 2022 Oct;57(10):2549-2552. doi: 10.1002/ppul.26063. Epub 2022 Jul 12.
No abstract available

Publication types

  • Letter
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Aminophenols / therapeutic use
  • Aminopyridines / therapeutic use
  • Benzodioxoles / therapeutic use
  • Child, Preschool
  • Cystic Fibrosis Transmembrane Conductance Regulator / genetics
  • Cystic Fibrosis* / complications
  • Cystic Fibrosis* / drug therapy
  • Drug Combinations
  • Humans
  • Mutation
  • Pneumonia*
  • Quinolones

Substances

  • Aminophenols
  • Aminopyridines
  • Benzodioxoles
  • Drug Combinations
  • Quinolones
  • Cystic Fibrosis Transmembrane Conductance Regulator
  • ivacaftor
  • lumacaftor