Background: Vascular abnormalities, including dissections and aneurysms, can be found in patients with autosomal dominant kidney disease (ADPKD). While intracranial aneurysms have been reported in 10%-25% of ADPCKD, occurrences at other locations are exceedingly rare.
Method: This is a first case report of a patient with ADPCKD who presented with a rupture of the left external carotid artery pseudoaneurysm.
Conclusion: Rupture of a carotid artery aneurysm is rare with potentially high morbidity. An endovascular and surgical approach are effective strategies for successful management that depends on etiology, location, and surgeon experience.
Keywords: PKD1 or PKD2 polycystic kidney disease genes; autosomal dominant polycystic kidney disease; figure; transforming growth factor beta.