An isolated congenital absence of right pulmonary artery associated with pulmonary hypertension with coronary collaterals: A case report

Muhammed Demir; Serkan Akdağ; Muhammed Akif Deniz; Hakkı Şimşek

doi:10.1111/echo.15450

An isolated congenital absence of right pulmonary artery associated with pulmonary hypertension with coronary collaterals: A case report

Echocardiography. 2022 Oct;39(10):1367-1369. doi: 10.1111/echo.15450. Epub 2022 Sep 13.

Authors

Muhammed Demir¹, Serkan Akdağ², Muhammed Akif Deniz³, Hakkı Şimşek¹

Affiliations

¹ Department of Cardiology, Dicle University School of Medicine, Diyarbakir, Turkey.
² Department of Cardiology, Memorial Hospital, Diyarbakir, Turkey.
³ Department of Radiology, Dicle University School of Medicine, Diyarbakir, Turkey.

PMID: 36100814
DOI: 10.1111/echo.15450

Abstract

Unilateral absence of pulmonary artery (UAPA) resulting from a defect in the aortic arch's embryogenesis. Patients who survive into adulthood is rare. Herein, we presented a case of UAPA with pulmonary hypertension in a 49-year old female.

Keywords: congenital heart disease; coronary artery collaterals introduction; pulmonary artery agenesis.

Publication types

Case Reports

MeSH terms

Adult
Female
Heart Defects, Congenital* / complications
Humans
Hypertension, Pulmonary* / complications
Lung / blood supply
Lung Diseases* / complications
Middle Aged
Pulmonary Artery / abnormalities
Pulmonary Artery / diagnostic imaging
Vascular Malformations* / complications