Craniosynostosis and hydrocephalus

Neurosurgery. 1987 Jul;21(1):63-7. doi: 10.1227/00006123-198707000-00013.


Ten cases of craniosynostosis associated with hydrocephalus were found in a retrospective review of 250 cases of children with craniosynostosis. Four children had Pfeiffer's syndrome, 3 had Crouzon's syndrome, 2 had kleeblattschädel with multiple anomalies and therefore could not be classified into a definite syndrome, and 1 had isolated sagittal synostosis. Of these 10 children, 5 had kleeblattschädel, two with Crouzon's syndrome, one with Pfeiffer's syndrome, and 2 with multiple anomalies. In all patients, hydrocephalus was controlled by a shunting procedure. Possible causes of hydrocephalus in association with craniosynostosis are discussed.

MeSH terms

  • Adolescent
  • Cerebrospinal Fluid Shunts
  • Child
  • Child, Preschool
  • Craniofacial Dysostosis / surgery
  • Craniosynostoses / surgery*
  • Follow-Up Studies
  • Humans
  • Hydrocephalus / congenital
  • Hydrocephalus / surgery*
  • Infant
  • Infant, Newborn
  • Syndrome