IgG4-related disease associated with the primary manifestation of recurrent cerebral venous thrombosis: A rare case report

Arsh Haj Mohamad Ebrahim Ketabforoush; Mahsa Bahadorinia; Elahe Dolatshahi; Zohreh Nozarian; Nahid Abbasi Khoshsirat

doi:10.1002/ccr3.6324

IgG4-related disease associated with the primary manifestation of recurrent cerebral venous thrombosis: A rare case report

Clin Case Rep. 2022 Sep 14;10(9):e6324. doi: 10.1002/ccr3.6324. eCollection 2022 Sep.

Authors

Arsh Haj Mohamad Ebrahim Ketabforoush¹, Mahsa Bahadorinia², Elahe Dolatshahi³, Zohreh Nozarian⁴, Nahid Abbasi Khoshsirat⁵

Affiliations

¹ Cellular and Molecular Research Center Iran University of Medical Sciences Tehran Iran.
² Student Research Committee Alborz University of Medical Sciences Karaj Iran.
³ Department of Rheumatology Clinical Research Development Unit (CRDU) of Shahid Rajaei Hospital Alborz University of Medical Sciences Karaj Iran.
⁴ Department of Pathology Farabi Eye Hospital Tehran University of Medical Sciences Tehran Iran.
⁵ Department of Neurology Clinical Research Development Unit (CRDU) of Shahid Rajaei Hospital Alborz University of Medical Sciences Karaj Iran.

Abstract

Nervous system involvement in IgG4-related systemic disease (IgG4-RD) is rarely reported and manifests as hypertrophic pachymeningitis and hypophysitis. In this report, a 33-year-old woman with neurological manifestations was diagnosed with IgG4-RD by biopsy. The patient showed improvement in symptoms after treatment.

Keywords: IgG4‐related disease; cerebral venous thrombosis; pachymeningitis.

Publication types

Case Reports