Multifocal Paraganglioma in Teenager Presenting With Hypertension

Urology. 2023 Feb:172:192-195. doi: 10.1016/j.urology.2022.10.006. Epub 2022 Oct 22.

Abstract

Pediatric hypertension represents a rare though increasingly common medical problem. When encountered, a workup to determine the etiology should be conducted. In this report, we detail an unusual case in which a teenager presenting with hypertension was found to have multifocal primary paragangliomas. We illustrate important considerations in management which include appropriate preoperative labs and imaging, collaboration with endocrinology for preoperative alpha-blockade, surgical management with close perioperative hemodynamic control, and genetic evaluation for all patients with paragangliomas.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Adrenal Gland Neoplasms* / surgery
  • Child
  • Diagnostic Imaging
  • Humans
  • Hypertension* / complications
  • Paraganglioma* / complications
  • Paraganglioma* / diagnosis
  • Paraganglioma* / genetics