A case of febrile ulceronecrotic Mucha-Habermann disease responsive to systemic corticosteroids

Pediatr Dermatol. 2023 May-Jun;40(3):573-575. doi: 10.1111/pde.15234. Epub 2022 Dec 27.

Abstract

Febrile ulceronecrotic Mucha-Habermann disease (FUMHD) is a rare, potentially fatal subtype of pityriasis lichenoides et varioliformis acuta (PLEVA). Herein, we present a rare case of a 14-year-old male without significant past medical history who was diagnosed with FUMHD without a clear inciting factor. He was effectively treated with systemic corticosteroids with complete resolution of symptoms.

Keywords: FUMHD; Mucha-Habermann; PLEVA; pityriasis lichenoides et varioliformis acuta.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Adrenal Cortex Hormones
  • Herpes Simplex*
  • Humans
  • Male
  • Pityriasis Lichenoides* / diagnosis
  • Pityriasis Lichenoides* / drug therapy

Substances

  • Adrenal Cortex Hormones

Supplementary concepts

  • Febrile Ulceronecrotic Mucha-Habermann disease