Tetralogy of Fallot with absent pulmonary valve in an adult

Indian J Thorac Cardiovasc Surg. 2023 Mar;39(2):198-200. doi: 10.1007/s12055-022-01407-1. Epub 2022 Aug 31.


Absent pulmonary valve syndrome (APVS) is seen in around 3 to 6% of tetralogy of Fallot (TOF) patients. They present in the neonatal or infantile period with respiratory compromise, cardiac failure, or cyanosis. They rarely survive into adulthood with only few reports published in literature so far. In this report, we present an adult patient with TOF and APVS, who underwent a successful repair with prosthetic valve implantation.

Keywords: Absent pulmonary valve; Bronchial compression; Prosthetic valve; Tetralogy of fallot.