MR imaging in a case of Hallervorden-Spatz disease

J Comput Assist Tomogr. 1987 Nov-Dec;11(6):1057-8. doi: 10.1097/00004728-198711000-00027.


Magnetic resonance using a 0.5 T system and a T2-weighted spin-echo pulse sequence revealed symmetric areas of marked hypointensity of the globi pallidi in a case with a family history of and presenting with clinical features consistent with Hallervorden-Spatz disease. No such findings were seen in any of 16 normal volunteers of similar age. Magnetic resonance may be useful for diagnosing Hallervorden-Spatz disease.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Basal Ganglia Diseases / diagnosis*
  • Globus Pallidus / pathology
  • Humans
  • Magnetic Resonance Imaging*
  • Male
  • Pantothenate Kinase-Associated Neurodegeneration / diagnosis*
  • Pantothenate Kinase-Associated Neurodegeneration / genetics