Motor band sign in a Huntington disease phenocopy

Parkinsonism Relat Disord. 2023 Apr:109:105333. doi: 10.1016/j.parkreldis.2023.105333. Epub 2023 Feb 20.


We report a 68-year-old lady who presented with Huntington phenocopy with generalized chorea and was genetically proven to have Spinocerebellar ataxia (SCA)17. MRI Brain demonstrated motor band sign, which is most commonly reported in motor neuron disease. This is the first case of motor band sign with SCA 17 and highlights the widening spectrum of radiological signs in SCA 17.

Keywords: Huntington disease phenocopy; MRI Brain; Motor band sign; SCA 17.

Publication types

  • Case Reports
  • Letter

MeSH terms

  • Aged
  • Chorea* / diagnostic imaging
  • Chorea* / etiology
  • Female
  • Humans
  • Huntington Disease* / complications
  • Huntington Disease* / diagnostic imaging
  • Motor Neuron Disease* / diagnostic imaging
  • Spinocerebellar Ataxias* / diagnosis

Supplementary concepts

  • Spinocerebellar Ataxia 17