Malignant metastatic steroid cell tumor NOS: A rare presentation of a subtype of sex cord stromal tumor

Sahana Punneshetty; Ajit Sebastian; Vinotha Thomas; Sherin Daniel; Priyaroseni Briskala; Ashish Singh; Anitha Thomas

doi:10.1016/j.gore.2023.101169

Malignant metastatic steroid cell tumor NOS: A rare presentation of a subtype of sex cord stromal tumor

Gynecol Oncol Rep. 2023 Mar 29:46:101169. doi: 10.1016/j.gore.2023.101169. eCollection 2023 Apr.

Authors

Sahana Punneshetty¹, Ajit Sebastian¹, Vinotha Thomas¹, Sherin Daniel², Priyaroseni Briskala¹, Ashish Singh³, Anitha Thomas¹

Affiliations

¹ Department of Gynaecologic Oncology, Christian Medical College, Vellore, Tamil Nadu, India.
² Department of General Pathology, Christian Medical College, Vellore, Tamil Nadu, India.
³ Department of Medical Oncology, Christian Medical College, Vellore, Tamil Nadu, India.

Abstract

Steroid cell tumors - not otherwise specified (NOS) - are rare sex cord stromal tumors that lack characteristic histology, are benign, and usually present with androgenic manifestations. Metastatic malignant steroid cell tumors pose treatment challenges due to their chemoresistance nature. This is a case report of a metastatic steroid cell tumor - NOS with extensive peritoneal disease.

Keywords: Adjuvant treatment; Hyperandrogenism; Steroid cell tumor.