[Acute posterior multifocal placoid pigment epitheliopathy, serpiginous choroiditis and related diseases]

Abstract

Acute Posterior Multifocal Placoid Pigment Epitheliopathy (APMPPE) and serpiginous choroiditis are two diseases classified as "white spot syndromes." Both are inflammatory/autoimmune diseases with suspected primary involvement of the choriocapillaris. The former usually has an excellent prognosis, while the latter can rapidly induce legal blindness. Whereas these diseases are well defined and well known, other entities (such as persistent placoid maculopathy or ampiginous choroiditis) with features of both APMPPE and serpiginous choroiditis have been described more recently. This review aims to describe demographic characteristics and multimodal imaging features to help differentiate between these four diseases.

Keywords: APMPPE; Acute posterior multifocal placoid pigment epitheliopathy; Ampiginous choroiditis; Choroïdite ampigineuse; Choroïdite serpigineuse; Maculopathie placoïde persistante; Persistant placoid maculopathy; Relentless placoid chorioretinitis; Serpiginous choroïdopathy; Syndrome des taches blanches; Épithéliopathie en plaque.