Flocculus Herniation into the Internal Acoustic Canal in Incomplete Partition Type I: A Case Report

J Int Adv Otol. 2023 Jun;19(3):266-268. doi: 10.5152/iao.2023.22797.

Abstract

In this study, we present the first case with cerebellar herniation into the internal acoustic canal in incomplete partition type I anomaly. Cerebellar herniation into the internal acoustic canal is very rare with only a few cases reported in the literature. Although it is a rare clinical situation, cerebellar herniation into the internal acoustic canal may be seen in patients with incomplete partition type I. We presented magnetic resonance imaging findings of a 3-year-old girl with a history of meningitis, middle ear effusion, and bilateral congenital sensorineural hearing loss. Magnetic resonance imaging showed bilateral incomplete partition type I malformation and an additional flocculus herniation into the right internal acoustic canal. In the presented case, predisposition to cerebrospinal fluid leak in incomplete partition type I anomaly may be the reason for cerebellar herniation into internal acoustic canal. Also, possible increased intracranial pressure due to meningitis may be a contributing factor.

Publication types

  • Case Reports

MeSH terms

  • Child, Preschool
  • Ear, Inner* / abnormalities
  • Encephalocele / diagnostic imaging
  • Encephalocele / surgery
  • Female
  • Hearing Loss, Bilateral
  • Hearing Loss, Sensorineural* / pathology
  • Humans
  • Magnetic Resonance Imaging
  • Tomography, X-Ray Computed / methods