Ecchordosis Physaliphora: Does It Even Exist?

AJNR Am J Neuroradiol. 2023 Aug;44(8):889-893. doi: 10.3174/ajnr.A7932. Epub 2023 Jul 13.

Abstract

The term ecchordosis physaliphora (EP) has been used historically to describe a benign notochordal remnant with no growth potential, most commonly occuring in the central clivus. Unfortunately, the radiologic appearance of EP overlaps considerably with the appearance of low-grade chordomas, which do have the potential for growth. In this article, we review new pathologic terminology that better describes this family of diseases, and we propose new radiologic terms that better address the uncertainty of the radiologic diagnosis. The surgical importance of accurate terminology and the implications for patient care are discussed.

Publication types

  • Review

MeSH terms

  • Cerebellar Vermis*
  • Chordoma* / diagnostic imaging
  • Chordoma* / pathology
  • Cranial Fossa, Posterior / diagnostic imaging
  • Cranial Fossa, Posterior / surgery
  • Humans
  • Notochord / pathology