Aortic Dissection in a Young Patient With Unsuspected Aortopathy

Pediatrics. 2023 Aug 1;152(2):e2022057694. doi: 10.1542/peds.2022-057694.


Aortic dissection is often a fatal condition if not recognized and treated emergently. Fortunately, it is extremely rare in children and adolescents. We report a case of an adolescent boy who survived an aortic dissection due to severe aortic root dilation. A comprehensive history and physical examination, including family history, can facilitate an early diagnosis of connective tissue diseases, such as Loeys-Dietz syndrome (LDS).