[Advances in IgG4-related hypertrophic pachymeningitis]

Zhonghua Nei Ke Za Zhi. 2023 Sep 1;62(9):1139-1143. doi: 10.3760/cma.j.cn112138-20220908-00668.
[Article in Chinese]

Abstract

IgG4相关性硬脑膜炎(IgG4-RHP)过去很大一部分被归入特发性肥厚性硬脑膜炎,现已证实IgG4-RHP实际为IgG4相关性疾病,一旦确诊应用糖皮质激素会使病情得到显著缓解。临床实践中,IgG4-RHP诊断困难、误诊及漏诊率较高,本文对IgG4-RHP相关研究进展作一综述,以期提高临床医生对IgG4-RHP的理解及认识。.

MeSH terms

  • Humans
  • Hypertrophy
  • Immunoglobulin G*

Substances

  • Immunoglobulin G