Pleural-based giant solitary fibrous tumour with associated hypoglycaemia: unusual presentation with pulmonary hypertension in a patient with Doege-Potter syndrome

Clin Med (Lond). 2023 Sep;23(5):518-520. doi: 10.7861/clinmed.2023-0274.

Abstract

Refractory hypoglycaemia in a patient with a solitary fibrous tumour (SFT) is very rare and was first reported in 1930 independently by Doege and Potter, leading to it being named 'Doege-Potter syndrome'. Here, we report the unusual case of a 77-year-old woman with a giant solitary fibrous pleural tumour who presented with complicating pulmonary hypertension and associated heart failure with hypoglycaemia, and subsequently underwent curative resection of the pleural mass with clinical improvement.

Keywords: Doege–Potter syndrome; hypoglycaemia; solitary fibrous tumour.

Publication types

  • Case Reports

MeSH terms

  • Aged
  • Female
  • Humans
  • Hypertension, Pulmonary* / etiology
  • Hypoglycemia* / etiology
  • Solitary Fibrous Tumor, Pleural* / diagnosis
  • Solitary Fibrous Tumor, Pleural* / diagnostic imaging
  • Syndrome

Supplementary concepts

  • Hereditary renal agenesis
  • Renal Adysplasia